weber-christian disease in a 9 month old boy: report of a case

نویسندگان

mamishi s

mojtahedi sy

mahjoub f

چکیده

idiopathic lobular panniculitis, sometimes called relapsing febrile nodular panniculitis or weber christian disease first desribed in 1892 by pfeifer, is the term used to describe an group of disease that present as subcutaneous inflammatory nodules and histologically display an inflammatory focus primarily within the fat lobules. weber-christian disease is the term applied to idiopatic cases of lobular panniculitis associated with systemic symptoms.the disease occurs predominantly in middle aged females although it can be seen in both sexes and at all ages. hereby, we represent a case of diagnosed weber-christian disease in a 9-month-old boy. the diagnosis was approved by skin biopsy and exclusion of other differential diagnosis of lobular panniculitis. weber-christian disease is a rare disease especially in children and can be misdiagnosed, so we found it interesting to report this case.

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عنوان ژورنال:
acta medica iranica

جلد ۴۰، شماره ۱، صفحات ۱۶-۱۹

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